Outpatient Nursing Care For Cystic Fibrosis Patients

Ana Cristina Almeida Moura, Dirce Nascimento Pinheiro

Abstract


Objective: to analyze the scientific evidence of outpatient nursing care for patients with cystic fibrosis. Method: this is a descriptive, bibliographic study, of the type integrative literature review, carried out with 14 articles available online, published from 2013 to 2017 in MEDLINE database, CINAHL, LILACS, BDENF, IBECS, and WEB OF SCIENCE. Data were analyzed according to the Content Analysis technique and were presented in figures. Results: the findings pointed that that the outpatient nursing care for cystic fibrosis patients is still incipient. There are difficulties in drug adherence, pain control, lack of involvement of families in the treatment, and decreased quality of life and comfort of patients. Conclusion: international articles mainly published in English and with level of evidence VI were observed, and there were more productions about cystic fibrosis in the pediatric area. It is understood that the themes that will contribute to the advancement of nursing in future studies are: medication adherence for treatment of cystic fibrosis; family-centered care; psychosocial support to clients and families; quality of life; and promotion of comfort; and pain relief. Descriptors: Cystic Fibrosis; Nursing care; Chronic Disease; Pneumology; Genetics; Nursing.

RESUMO

Objetivo: analisar as evidências científicas acerca dos cuidados de Enfermagem no âmbito ambulatorial voltados aos pacientes com fibrose cística. Método: trata-se de estudo descritivo, bibliográfico, tipo revisão integrativa, com 14 artigos disponíveis on-line, no período de 2013 a 2017, nas bases de dados MEDLINE, CINAHL, LILACS, BDENF, IBECS, WEB OF SCIENCE, analisados pela Técnica de Análise de Conteúdo, e apresentados em forma de figuras. Resultados: avalia-se que a assistência de Enfermagem no ambulatório ao paciente com fibrose cística ainda é incipiente; com isto, há dificuldades na adesão medicamentosa, controle da dor, falta de envolvimento da família no tratamento, diminuição da qualidade de vida e conforto do paciente. Conclusão: observou-se uma literatura internacional constituída, majoritariamente, por produções em inglês, com nível de evidência VI, e percebeu-se que há mais produções sobre a fibrose cística na área pediátrica. Entende-se que os temas que contribuirão para o avanço da Enfermagem em estudos futuros serão: a adesão medicamentosa ao tratamento para a fibrose cística; os cuidados centrados na família; o apoio psicossocial ao cliente e família; a qualidade de vida; a promoção do conforto e o alívio da dor. Descritores: Fibrose Cística; Cuidados de Enfermagem; Doença Crônica; Pneumologia; Genética; Enfermagem.  

RESUMEN

Objetivo: analizar las evidencias científicas acerca de los cuidados de Enfermería en el ámbito ambulatorial dirigidos a los pacientes con fibrosis cística. Método: se trata de un estudio, descriptivo, bibliográfico, tipo revisión integradora de la literatura, con 14 artículos disponibles on-line, en el período de 2013 a 2017, en las bases de datos MEDLINE, CINAHL, LILACS, BDENF, IBECS, WEB OF SCIENCE, estudiados según el Análisis de Contenido y presentados en forma de figuras. Resultados: se evalúa que la asistencia de Enfermería en el ambulatorio al paciente con fibrosis cística aún es incipiente, con eso hay dificultades en la adhesión medicamentosa, control del dolor, falta de envolvimiento de la familia en el tratamiento, disminución de la calidad de vida y confort del paciente. Conclusión: se observó una literatura internacional constituida mayoritariamente por producciones en inglés, con nivel de evidencia VI, y se percibe que hay más producciones sobre la fibrosis cística en el área pediátrica. Se entiende que los temas que contribuirán para el avance de la Enfermería en estudios futuros serán la adhesión medicamentosa al tratamiento para la fibrosis cística; los cuidados centrados en la familia; el apoyo psicosocial al cliente y familia; la calidad de vida; la promoción del confort; y el alivio del dolor. Descriptores: Fibrosis Quística; Atención de Enfermería; Enfermedad Crónica; Neumología; Genética; Enfermería.


Keywords


Fibrose cística; Cuidados de enfermagem; Doença Crônica; Pneumologia; Genética; Enfermagem

References


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DOI: https://doi.org/10.5205/1981-8963.2019.238157



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